#ht1

#FlashbackFriday to almost 5 years ago with my now long-gone 1966 #Gibson #ES330 TDC. Wish I didn’t have to sell that one. You can also see my one and only acoustic, a #Martin #0018V (now owned by @tomgibson3783) plus the #Epiphone #Wilshire Reissue (purchased from @rumbleseatmusic when they were in Ithaca NY) and #Casino Coupe (also long-gone). Proto-#ToneHenge™ included my @blackstaramps #HT1 RH, 1957 #Fender #Champ (now owned by @the_damo_experience), @marshallamps_uk JTM1C (sold to @michaelsegui) and 1968 Fender #VibroChamp (now owned by @malonzi5150). #fbf #vintageamp #fenderamp #guitar #guitars #guitarra #chitarra #guitarre #electricguitar #vintageguitars #vintagegibson #gibsonguitars #guitarsdaily #vintagegear #gibsonsofinstagram #guitarphotography https://www.instagram.com/p/Bvm12yWh8g6/?utm_source=ig_tumblr_share&igshid=1i263kuqrpsuw

//// You never forget your first. We have so many people telling us the HT-1 was their dream bike as a kid. What was your first bike?

Before she knew it, her feet had already taken her to the single set of half-opened doors and she dared to peek inside, only to be blown away by the sight of a powerful jump serve that left her heart racing. 

Flashback to my first #Gibson ES ever, this 2011-ish CustomShop #ES330 “L” (called L because it has the longer neck like the post-1967 330s had). Also can you dig #ToneHenge™ 2012?? 2 #amps only! 😀 A 4 watt Mack Gem and a 1 watt @blackstaramps #HT1 RH. #blackstaramps #tbt #throwback #guitarcollection #guitar #guitars #guitarra #chitarra #guitarre #electricguitar #gibsoncustom #customshop #reissue #gibsonguitars #tone #guitargear #guitarsdaily #guitarsofinstagram #geartalk #guitargear #vintagegear #guitarsdaily #gibsonsofinstagram #guitarphotography (at Toronto, Ontario) https://www.instagram.com/p/Bu_voV_A-KP/?utm_source=ig_tumblr_share&igshid=i1k9gnzd4smz

//// “Ride Fast” in the new ‘Charlotte’ coach’s jacket because even a 90 can feel fast. Peek them at onedownfourup.us.

Special formulas are carefully designed nutritional products created to meet the unique dietary needs of individuals with medical conditions, metabolic disorders, or nutritional deficiencies. These formulas provide balanced nutrients while restricting harmful components that the body may not process properly. Commonly used in therapeutic nutrition and rare disease management, special formulas support growth, metabolic stability, and overall health. Under medical supervision, they help improve treatment outcomes, maintain nutritional balance, and provide essential support for patients requiring long-term specialized dietary care.

Hereditary Tyrosinemia Type 1 (HT1) is a rare genetic disorder that affects how the body breaks down the amino acid tyrosine. This condition is caused by a mutation in the FAH gene, leading to a deficiency of the enzyme fumarylacetoacetate hydrolase (FAH). Without this enzyme, toxic by-products build up in the body, causing serious health problems.

The diagnosis of Tyrosinemia Type 1 involves a comprehensive clinical assessment and specialized tests. Early indicators often include failure to thrive and hepatomegaly. Definitive diagnosis typically involves detecting specific tyrosine metabolites and succinylacetone in urine samples. Measuring FAH enzyme activity in liver tissue or conducting molecular genetic testing for FAH gene mutations confirms the diagnosis. Newborn screening programs measuring succinylacetone in blood spots have also proven effective in early detection, facilitating timely intervention.